D81 | Combined immunodeficiencies |
| Severe combined immunodeficiency [SCID] with reticular dysgenesis |
| Severe combined immunodeficiency [SCID] with low T- and B-cell numbers |
| Severe combined immunodeficiency [SCID] with low or normal B-cell numbers |
| Adenosine deaminase [ADA] deficiency |
| Adenosine deaminase deficiency, unspecified |
| Severe combined immunodeficiency due to adenosine deaminase deficiency |
| Adenosine deaminase 2 deficiency |
| Other adenosine deaminase deficiency |
| Nezelof’s syndrome |
| Purine nucleoside phosphorylase [PNP] deficiency |
| Major histocompatibility complex class I deficiency |
| Major histocompatibility complex class II deficiency |
| Other combined immunodeficiencies |
| Biotin-dependent carboxylase deficiency |
| Biotinidase deficiency |
| Other biotin-dependent carboxylase deficiency |
| Biotin-dependent carboxylase deficiency, unspecified |
| Other combined immunodeficiencies |
| Combined immunodeficiency, unspecified |