D81.- Combined immunodeficiencies

Excludes

  • Autosomal recessive agammaglobulinemia (Swiss type) (D80.0)
  • D81
  • Combined immunodeficiencies
    • D81.0
    Severe combined immunodeficiency [SCID] with reticular dysgenesis
    • D81.1
    Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
    • D81.2
    Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
    • D81.3
    Adenosine deaminase [ADA] deficiency
      • D81.30
    Adenosine deaminase deficiency, unspecified
      • D81.31
    Severe combined immunodeficiency due to adenosine deaminase deficiency
      • D81.32
    Adenosine deaminase 2 deficiency
      • D81.39
    Other adenosine deaminase deficiency
    • D81.4
    Nezelof’s syndrome
    • D81.5
    Purine nucleoside phosphorylase [PNP] deficiency
    • D81.6
    Major histocompatibility complex class I deficiency
    • D81.7
    Major histocompatibility complex class II deficiency
    • D81.8
    Other combined immunodeficiencies
      • D81.81
    Biotin-dependent carboxylase deficiency
          • D81.810
    Biotinidase deficiency
          • D81.818
    Other biotin-dependent carboxylase deficiency
          • D81.819
    Biotin-dependent carboxylase deficiency, unspecified
      • D81.89
    Other combined immunodeficiencies
    • D81.9
    Combined immunodeficiency, unspecified